Anesthetic management of a patient with prune-belly syndrome : A case report

Hwang, Bo Young; Kim, Yoo Kyung; Park, Ji Hyun; Park, Joon Young; Seo, Young Joo; Bang, Ji Yeon; Jeong, Sung Moon; Hwang, Jai Hyun

Case Report

Pediatric Anesthesia

Anesthesia and Pain Medicine 2009;4(1):50-54.
Published online January 30, 2009.

Anesthetic management of a patient with prune-belly syndrome : A case report

Bo Young Hwang, Yoo Kyung Kim, Ji Hyun Park, Joon Young Park, Young Joo Seo, Ji Yeon Bang, Sung Moon Jeong, Jai Hyun Hwang

Department of Anesthesiology and Pain Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. avnhip@hanmail.net

Abstract

Prune-belly syndrome is characterized by absent abdominal wall musculature with wrinkled overlying skin, urinary tract dilatation and cryptorchidism. Prune-belly syndrome is also associated with diseases of the respiratory, cardiovascular, skeletal, gastrointestinal and central nervous system. Because the congenital disease is uncommon, it is difficult to collect the information of anesthetic management of prune-belly syndrome. We report a case of 4 year-old-boy with prune-belly syndrome who underwent abdominoplasty and Mitrofanoff operation under general anesthesia.

Key Words: general anesthesia, prune-belly syndrome