An Anesthetic Experience for Russell-SilverSyndrome : A case report

Yoo, Tae Joong; Lee, Sang Seok; Lim, Yeun Hee; Yoo, Byung Hoon; Woo, Seung Hoon

Case Report

Pediatric Anesthesia

Anesthesia and Pain Medicine 2006;1(1):64-67.
Published online July 30, 2006.

An Anesthetic Experience for Russell-SilverSyndrome : A case report

Tae Joong Yoo, Sang Seok Lee, Yeun Hee Lim, Byung Hoon Yoo, Seung Hoon Woo

Department of Anesthesiology and Pain Medicine, Sanggye Paik Hospital, College of Medicine, Inje University, Seoul, Korea. sslee@sanggyepaik.ac.kr

Abstract

We present a 4-years-old Russell-Silver syndrome patient who underwent surgical correction of left auricular abnormality. He had a triangular face with hypoplastic mandible. Because of facial manifestations of this syndrome, the anesthesiologist should prepare for a difficult endotracheal intubation and mask fitting. These patients may be prone especially to hypoglycemia and hypothermia during intraoperative period, therefore close monitoring and appropriate care for hypoglycemia and hypothermia is required. In this case, gentle direct laryngoscopy was performed to assess the airway. Hypoglycemia and hypothermia was not observed. We discuss anesthetic considerations in management.

Key Words: anesthesia, intubation, pediatric, Russell-Silver syndrome